Genetic, structural and clinical analysis of spastic paraplegia 4.

Varghaei P, Estiar MA, Ashtiani S, Veyron S, Mufti KLeveille EYu E, Spiegelman D, Rioux MF, Yoon G, Tarnopolsky M, Boycott KM, Dupre N, Suchowersky O, Trempe JF, Rouleau GA and Gan-Or ZGenetic, structural and clinical analysis of spastic paraplegia 4Parkinsonism and Related Disorders. 2022. PubMed, Preprint

RABENOSYN separation-of-function mutations uncouple endosomal recycling from lysosomal degradation, causing a distinct Mendelian Disorder. 

Paul F, Ng C, Nafissi S, Nilipoor Y, Tavasoli A, Bonnard C, Wong PM, Nabavizadeh N, Estiar MA, Majoie C, Lee H, Nelson S, Gan-Or Z, Rouleau GA, Van Veldhoven P, Massie R, Hennekam R and Kariminejad A. RABENOSYN separation-of-function mutations uncouple endosomal recycling from lysosomal degradation, causing a distinct Mendelian Disorder. Human Molecular Genetics. 2022. PubMed, Preprint

Enrichment of SARM1 alleles encoding variants with constitutively hyperactive NADase in patients with ALS and other motor nerve disorders.

Gilley J, Jackson O, Pipis M, Estiar MA, Al-Chalabi A, Danzi MC, van Eijk KR, Goutman SA, Harms MB, Houlden H, Iacoangeli A, Kaye J, Lima L, Ravits J, Rouleau GA, Schüle R, Xu J, Züchner S, Cooper-Knock J, Gan-Or Z, Reilly MM and Coleman MP. Enrichment of SARM1 alleles encoding variants with constitutively hyperactive NADase in patients with ALS and other motor nerve disorders. eLife. 2021. PubMed, Preprint

Heterozygous de novo KPNA3 Mutations Cause Complex Hereditary Spastic Paraplegia.

Estiar MA, Lail N, Dyment DA, Varghaei P, Hartley T, Gillespie MK, Yoon G, Boycott KM, Rouleau GA and Gan-Or Z. Heterozygous de novo KPNA3 Mutations Cause Complex Hereditary Spastic ParaplegiaAnnals of Neurology. 2021. PubMed

Brain atrophy progression in Parkinson’s disease is shaped by connectivity and local vulnerability. 

Tremblay C, Rahayel S, Vo A, Morys F, Shafiei G, Markello R, Gan-Or Z, Misic B and Dagher A. Brain atrophy progression in Parkinson’s disease is shaped by connectivity and local vulnerabilityBrain Communications. 2021. PubMed, Preprint

New therapeutic approaches to Parkinson’s disease targeting GBA, LRRK2 and Parkin.

Senkevich KRudakou U and Gan-Or ZNew therapeutic approaches to Parkinson’s disease targeting GBA, LRRK2 and ParkinNeuropharmacology. 2021. PubMed

Plasma glucosylsphingosine in glucocerebrosidase carriers with and without Parkinson disease.

Surface M, Balwani M, Waters CH, Haimovich A, Gan-Or Z, Marder KS, Hsieh T, Song L, Padmanabhan S, Hsieh F, Merchant KM and Alcalay RN. Plasma glucosylsphingosine in glucocerebrosidase carriers with and without Parkinson diseaseMovement Disorders. 2021. PubMed

Hereditary spastic paraplegia initially diagnosed as cerebral palsy. 

Suchowersky O, Ashtiani S, Au PYB, McLeod S, Estiar MAGan-Or Z and Rouleau GA. Hereditary spastic paraplegia initially diagnosed as cerebral palsyClinical Parkinsonism & Related Disorders. 2021. PubMed

Rare PSAP variants and possible interaction with GBA in REM sleep behavior disorder. 

Sosero YLYu EEstiar MA, Mufti K, Rudakou URuskey JAAsayesh F, Laurent SB, Spiegelman D, Trempe JF, Quinnell TG, Oscroft N, Arnulf I, Montplaisir JY, Gagnon JF, Desautels A, Dauvilliers Y, Gigli GL, Valente M, Janes F, Bernardini A, Sonka K, Kemlink D, Oertel W, Janzen A, Plazzi G, Antelmi E, Biscarini F, Figorilli M, Puligheddu M, Mollenhauer B, Trenkwalder C, Sixel-Döring F, Cochen De Cock V, Monaca CC, Heidbreder A, Ferini-Strambi L, Dijkstra F, Viaene M, Abril B, Boeve BF, Postuma RB, Rouleau GA, Ibrahim A, Stefani A, Högl B, Hu MTM, and Gan-Or ZRare PSAP variants and possible interaction with GBA in REM sleep behavior disorderJournal of Parkinson’s Disease. 2021. PubMedPreprint

Genetic stratification of age-dependent Parkinson’s disease risk by polygenic hazard score.

Pihlstrøm L, Fan CC, Frei O, Tan M, Blauwendraat C, Bandres-Ciga S, Gan-Or Z, Grosset DG, International Parkinson’s Disease Genomics Consortium (IPDGC), Dale AM, Seibert TM and Andreassen OA. Genetic stratification of age-dependent Parkinson’s disease risk by polygenic hazard scoreMovement Disorders. 2021. PubMed